The Rising Double Heterozygous Cases of Haemoglobinopathies In Paediatric Population-A Hospital Based Cross Sectional Study
نویسندگان
چکیده
In this study various abnormal haemoglobin fractions on HPLC were observed in 158 cases out of the total 300 screened paediatric anaemic cases. Of the 300 paediatric cases, samples analyzed on CE-HPLC for haemoglobinopathies, maximum 67 (22.33%) cases were diagnosed as S-β double heterozygous, 39(13%) as sickle cell trait, 27 (9 %) as β-thalassaemia major, 10 (3.33 %) as sickle cell disease, 05 (1.66 %) were diagnosed as β-thalassaemia trait, 03 ( 1%) were unknown haemoglobins , 02 (0.66 %) as Hb E-β-thalassaemia double heterozygous, 02 (0.66 %) as SCT + Hb D trait and 01 (0.3%) as Hb E trait.
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